Identifiers
mitochondrially encoded NADH dehydrogenase 4L
HUGO:MT-ND4L HGNC:7460 ENTREZ:4539 UNIPROT:P03901 GENECARDS:MT-ND4L REACTOME:60614 WIKI:MT-ND4L
Maps_Modules
Apoptosis / MITOCH_METABOLISM
MT-ND4L@Mitochondrial inner membrane
References
a_re69( Apoptosis ):
PMID:16200211
NDUFAF2
PMID:17344420
ECSIT:NDUFAF1
PMID:20816094
involvement of ACAD9 in the ECSIT:NDUFAF1 complex
PMID:16218961
NDUFAF1
PMID:15526035
AIF deficient cells exhibit a decrease content of complex I. It was proposed that AIF has a role in the biogenesis or maintenance of complex I
PMID:20025615
comprehensive review about complex I
Modifications:
In compartment: Mitochondrial inner membrane
Participates in complexes:
In compartment: Mitochondrial inner membrane
- FMN:MT-ND1:MT-ND2:MT-ND3:MT-ND4:MT-ND4L:MT-ND5:MT-ND6:NDUFA1:NDUFA10:NDUFA11:NDUFA12:NDUFA13:NDUFA2:NDUFA3:NDUFA4:NDUFA5:NDUFA6:NDUFA7:NDUFA8:NDUFA9:NDUFAB1:NDUFB1:NDUFB10:NDUFB11:NDUFB2:NDUFB3:NDUFB4:NDUFB5:NDUFB6:NDUFB7:NDUFB8:NDUFB9:NDUFC1:NDUFC2:NDUFS1|[2Fe-2S],[4Fe-4S],[4Fe-4S]:NDUFS2:NDUFS3:NDUFS4:NDUFS5:NDUFS6:NDUFS7|[4Fe-4S]:NDUFS8|[4Fe-4S],[4Fe-4S]:NDUFV1|[4Fe-4S]:NDUFV2|[2Fe-2S]:NDUFV3@Mitochondrial inner membrane
Participates in reactions:
As Reactant or Product:
- rMT-ND4L@Mitochondrial Matrix
→
MT-ND4L@Mitochondrial inner membrane
- FMN:MT-ND1:MT-ND2:MT-ND3:MT-ND4:MT-ND4L:MT-ND5:MT-ND6:NDUFA1:NDUFA10:NDUFA11:NDUFA12:NDUFA13:NDUFA2:NDUFA3:NDUFA4:NDUFA5:NDUFA6:NDUFA7:NDUFA8:NDUFA9:NDUFAB1:NDUFB1:NDUFB10:NDUFB11:NDUFB2:NDUFB3:NDUFB4:NDUFB5:NDUFB6:NDUFB7:NDUFB8:NDUFB9:NDUFC1:NDUFC2:NDUFS1|[2Fe-2S],[4Fe-4S],[4Fe-4S]:NDUFS2:NDUFS3:NDUFS4:NDUFS5:NDUFS6:NDUFS7|[4Fe-4S]:NDUFS8|[4Fe-4S],[4Fe-4S]:NDUFV1|[4Fe-4S]:NDUFV2|[2Fe-2S]:NDUFV3@Mitochondrial inner membrane
→
cleaved~NDUFS3*@Mitochondrial intermembrane space
- FMN:MT-ND1:MT-ND2:MT-ND3:MT-ND4:MT-ND4L:MT-ND5:MT-ND6:NDUFA1:NDUFA10:NDUFA11:NDUFA12:NDUFA13:NDUFA2:NDUFA3:NDUFA4:NDUFA5:NDUFA6:NDUFA7:NDUFA8:NDUFA9:NDUFAB1:NDUFB1:NDUFB10:NDUFB11:NDUFB2:NDUFB3:NDUFB4:NDUFB5:NDUFB6:NDUFB7:NDUFB8:NDUFB9:NDUFC1:NDUFC2:NDUFS1|[2Fe-2S],[4Fe-4S],[4Fe-4S]:NDUFS2:NDUFS3:NDUFS4:NDUFS5:NDUFS6:NDUFS7|[4Fe-4S]:NDUFS8|[4Fe-4S],[4Fe-4S]:NDUFV1|[4Fe-4S]:NDUFV2|[2Fe-2S]:NDUFV3@Mitochondrial inner membrane
→
cleaved~NDUFS1*@Mitochondrial intermembrane space
- degraded + NDUFS8@Mitochondrial inner membrane
+ MT-ND5@Mitochondrial inner membrane
+ MT-ND4@Mitochondrial inner membrane
+ MT-ND4L@Mitochondrial inner membrane
+ MT-ND3@Mitochondrial inner membrane
+ MT-ND2@Mitochondrial inner membrane
+ MT-ND1@Mitochondrial inner membrane
+ MT-ND6@Mitochondrial inner membrane
→
FMN:MT-ND1:MT-ND2:MT-ND3:MT-ND4:MT-ND4L:MT-ND5:MT-ND6:NDUFA1:NDUFA10:NDUFA11:NDUFA12:NDUFA13:NDUFA2:NDUFA3:NDUFA4:NDUFA5:NDUFA6:NDUFA7:NDUFA8:NDUFA9:NDUFAB1:NDUFB1:NDUFB10:NDUFB11:NDUFB2:NDUFB3:NDUFB4:NDUFB5:NDUFB6:NDUFB7:NDUFB8:NDUFB9:NDUFC1:NDUFC2:NDUFS1|[2Fe-2S],[4Fe-4S],[4Fe-4S]:NDUFS2:NDUFS3:NDUFS4:NDUFS5:NDUFS6:NDUFS7|[4Fe-4S]:NDUFS8|[4Fe-4S],[4Fe-4S]:NDUFV1|[4Fe-4S]:NDUFV2|[2Fe-2S]:NDUFV3@Mitochondrial inner membrane
As Catalyser:
- ubiquinone@Mitochondrial inner membrane
+ H+@Mitochondrial Matrix
+ NADH@Mitochondrial Matrix
→
ubiquinol@Mitochondrial inner membrane
+ H+@Mitochondrial intermembrane space
+ NAD_super_+_endsuper_@Mitochondrial Matrix
- NADH@Mitochondrial Matrix
+ O_sub_2_endsub_@Mitochondrial Matrix
→
NAD_super_+_endsuper_@Mitochondrial Matrix
+ O_sub_2_endsub__super_-_endsuper_@Mitochondrial Matrix